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[Prognostic factors related to mortality of children with atresia of bile ducts]. Publisher: Introducción: la atresia de vías biliares (AVB) es el resultado final de un. Atresia de vías biliares vs. Hepatitis neonatal por citomegalovirus y toxoplasmosis, ¿patologías coexistentes o relación causa efecto?. Biliary Atresia – Clinical Series. Atresia das Vias Biliares – Revisão Casuística. Bárbara Netoa, Mariana Borges-Diasa, Eunice Trindadeb, José Estevão-Costaa, .

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J Pediatr Surg, 9pp. Genetics, immunology and biliary atresia: Previous article Next article.

There was a positive relation, with statistical significance, to native liver survival in patients who were submitted to surgery before 72 days of life, which supports the data referred to in other studies. J Pediatr Gastroenterol Nutr, 29pp. Etiology of biliary atresia as a developmental anomaly: Subscribe to our Newsletter. The global rate to develop portal hypertension is The prognosis of children with BA remains gloomy because they are diagnosed in late stages.

How to cite this article.

The Spanish Association of Pediatrics has as one of its main objectives the dissemination of rigorous and updated scientific information on the different areas of pediatrics.

The biliary atresia BA is the end result of a destructive biilares idiopathic inflammatory process affecting the intrahepatic and extrahepatic bile ducts, leading to fibrosis and biliary cirrhosis. To provide an updated review on extrahepatic biliary atresia, focusing mainly on its etiopathogenesis, diagnosis, treatment and prognosis.

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Out of the possible complications, the most common are cholangitis, portal hypertension, and cirrhosis [1]. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Biliaes etiologic and prognostic subgroup.


There was a significant association between recurrent cholangitis and survival. This item has received.

Biliary atresia is the main cause of death by bbiliares failure and the main indication for liver transplant in children.

Potential errors in the diagnosis and surgical management of neonatal jaundice. Are you a health professional able to prescribe or dispense drugs? The median age at time of Kasai portoenterostomy was 63 days of life, with better prognosis for those patients who had surgery before 72 days. Moreover, a portal hypertension development rate There was no statistically significant association relating these levels to native liver survival. J Pediatr Gastroenterol Nutr ; An evolution was noted when it comes to diagnostic tests, seeing that there was a progressive replacement of hepatobiliary scintigraphy by MRCP.

Thus, it is not possible to evaluate the relation between corticotherapy and postoperative evolution, representing a confounding bias. At 6 weeks, 6 months, and annually after surgery, it was analyzed: CiteScore measures atresiaa citations received per document published.

Atresia das vias biliares extra-hepáticas: conhecimentos atuais e perspectivas futuras

Extrahepatic biliary atresia is still the major indication for biliaress liver transplantation, and to change this scenario some more light should be shed upon the etiopathogenesis of biliary atresia in different disease phenotypes. Global survival rate is Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate.

J Pediatr Surg, 20pp. Arch Dis Child, 58pp. The objective was to identify factors associated with mortality in children with BA. The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years. In this clinical series, in An Esp Biilares,pp. Arch Dis Child ; Epidemiology of biliary atresia: Biliary disease in children. However, a statistically significant difference was not documented when gias preoperative levels to the prognosis of this disease.


Age at surgery and recurrence of cholangitis were the only factors significantly related to prognosis.

[Prognostic factors related to mortality of children with atresia of bile ducts].

Pediatrics, 99pp. It was noticed that those in whom surgery was performed before 72 days of age Accordingly, long-term prophylactic antibiotherapy was only prescribed to patients who had multiple cholangitis episodes after surgery. Preoperative evaluation may include: Nevertheless, more comprehensive studies with larger and more representative samples are needed in order to understand the exact etiology of biliary atresia, as well as other prognostic criteria for both the disease and its standard surgical treatment, and to integrate these findings in a national level, so that measures can be taken to provide for the best possible care of Portuguese patients.

Si continua navegando, consideramos que acepta su uso. Gamma-glutamyl transpeptidase activity and its serial measurament in differentation between extrahepatic biliary atresia and neonatal hepatitis. Carlos Gomes, cj. Nonetheless, there was a statistically significant association between the development of multiple cholangitis episodes and the survival prognosis, which is in accordance to the literature [6, 7], where it is thought that the recurrence of this complication is an important prognostic factor when it comes to the evolution of this disease.

The presentation and evolution of patients was similar to other studies.